Repositorio Dspace

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  • Miralles-López, Juan-Carlos; Carbonell-Martínez, Antonio; Zamarro-Parra, Soledad; Navarro-Garrido, Cristina; Escudero-Pastor, Ana-Isabel; Boulaich, Muna; Sanroman-Sirvent, Sol; Petryk-Petryk, Yulia; Ladrón-de-Guevara, María-Dolores; Pérez-Fernández, Virginia (CODON PUBLICATIONS, 2024)
    BACKGROUND: Allergy to lipid transfer proteins (LPT) is common in Mediterranean Europe, and it causes severe reactions in patients and affects multiple foods, impairing the quality of life. OBJECTIVE: This study aimed to ...
  • Muntañola, Ana; Villacampa, Guillermo; Hernández-Rivas, José-Ángel; Alonso, Rosalía; Mirás, Fátima; Osorio, Santiago; Baile, Mónica; Baltasar, Patricia; López-Jiménez, Javier; Hernández-Rodríguez, Inés; Valenciano, Susana; Alfayate, Ana; Gimeno, Eva; Bárez, Abelardo; Oliveira, Ana-C; Riaza, Rosalía; Romero, Pilar; Delgado, Julio; Yáñez, Lucrecia; Zabalza, Amaya; Torres, Ana; Gómez-Roncero, María-Isabel; Crespo, Marta; Córdoba, Raúl; Mateos-Mazón, Juan-José; Pérez, Sonia; Andreu, Rafael; Labrador, Jorge; Ruiz, María-Elena; Velasquez, César-Andrés; Terol, María-José; Santiago, Raquel; Vidal, María-Jesús; Campoy-García, Fiz; Villalón, Lucía; Muiña, Begoña-S; Soler, Joan-Alfons; Seri, Cristina; Sánchez, María-José; Cuesta, Amalia; Ramos, Rafael; Sánchez-Montalvá, Adrián; Ruiz-Camps, Isabel; González, Marcos; Abrisqueta, Pau; Bosch, Francesc (BioMed Central Ltd, 2020)
  • Carriqui-Arenas, Sonia; Mosquera, Juan-Manuel; Quesada-Masachs, Estefania; López, Mireia; Clemente, Daniel; Boteanu, Alina; Udaondo, Clara; de-Inocencio, Jaime; Nieto, Juan-Carlos; Riancho, Leyre; Nunez, Esmeralda; Sánchez-Manubens, Judith; Lirola, María-José; Roldan, Rosa; Camacho, Marisol; Martínez, Melania; Medrano, Marta; Alcaniz, Paula; Anton, Jordi; Iglesias, Estibaliz (BMC, 2024-07)
    BACKGROUND: Juvenile Dermatomyositis (JDM) is the most common chronic idiopathic inflammatory myopathy in children. The diagnosis is clinical. Baseline laboratory and complementary studies trace the phenotype of these ...
  • Bain, Robert; Cosgriff, Rebecca; Zampoli, Marco; Elbert, Alexander; Burgel, Pierre-Regis; Carr, Siobhan-B; Castanos, Claudio; Colombo, Carla; Corvol, Harriet; Faro, Albert; Goss, Christopher-H; Gutiérrez, Hector; Jung, Andreas; Kashirskaya, Nataliya; Marshall, Bruce-C; Melo, Joel; Mondéjar-López, Pedro; Monestrol, Isabelle-de; Naehrlich, Lutz; Padoan, Rita; Pastor-Vivero, María-Dolores; Rizvi, Samar; Salvatore, Marco; Ribeiro-Ferreira-da-Silva-Filho, Luiz-Vicente; Brownlee, Keith-G; Haq, Iram-J; Brodlie, Malcolm (ELSEVIER, 2021-01)
    BACKGROUND: The presence of co-morbidities, including underlying respiratory problems, has been identified as a risk factor for severe COVID-19 disease. Information on the clinical course of SARS-CoV-2 infection in children ...
  • Romiti, Giulio-Francesco; Proietti, Marco; Vitolo, Marco; Bonini, Niccolo; Fawzy, Ameenathul-Mazaya; Ding, Wern-Yew; Fauchier, Laurent; Marín, Francisco; Nabauer, Michael; Dan, Gheorghe-Andrei; Potpara, Tatjana-S; Boriani, Giuseppe; Lip, Gregory-YH (BMC, 2022-09)
    BACKGROUND: Clinical complexity is increasingly prevalent among patients with atrial fibrillation (AF). The 'Atrial fibrillation Better Care' (ABC) pathway approach has been proposed to streamline a more holistic and ...
  • Jiménez-Yuste, Víctor; Teresa-Álvarez-Roman, María; Palomo-Bravo, Ángeles; Galmes, Bernardo-J; Nieto-Hernández, María-del-Mar; Benitez-Hidalgo, Olga; Marzo-Alonso, Cristina; Pérez-González, Noelia-Florencia; Coll, Julia; Nunez, Ramiro; Carrasco, Marina; García-Candel, Faustino; González-Porras, José-Ramón; Hernández-García, Carmen; Varo-Castro, María-José; Mir, Roser (SAGE PUBLICATIONS INC, 2022-02)
    OBJECTIVE: To evaluate the efficacy and safety of a plasma-derived factor VIII concentrate containing von Willebrand Factor (pdVWF/FVIII) in standard clinical practice in von Willebrand Disease (VWD) patients. METHODS: A ...
  • Ferrer, María-D; Sánchez-Barrueco, Álvaro; Martínez-Beneyto, Yolanda; Mateos-Moreno, María, V; Ausina-Marquez, Verónica; García-Vázquez, Elisa; Puche-Torres, Miguel; Forner-Giner, María-J; Campos-González, Alfonso; Santillan-Coello, Jessica-M; Alcala-Rueda, Ignacio; Villacampa-Auba, José-M; Cenjor-Espanol, Carlos; López-Velasco, Ana; Santolaya-Abad, Diego; García-Esteban, Sandra; Artacho, Alejandro; López-Labrador, Xavier; Mira, Alex (NATURE PORTFOLIO, 2021-12-22)
    Most public health measures to contain the COVID-19 pandemic are based on preventing the pathogen spread, and the use of oral antiseptics has been proposed as a strategy to reduce transmission risk. The aim of this manuscript ...
  • Quijada-Fraile, Pilar; Arranz-Canales, Elena; Martín-Hernández, Elena; Ballesta-Martínez, María-Juliána; Guillén-Navarro, Encarna; Pintos-Morell, Guillem; Molto-Abad, Marc; Moreno-Martínez, David; García-Morillo, Salvador; Blasco-Alonso, Javier; Luz-Couce, María; Gil-Sánchez, Ricardo; Cortes-Saladelafont, Elisenda; López-Rodríguez, Mónica-A; García-Silva, María-Teresa; Morales-Conejo, Montserrat (BMC, 2021-11)
    BACKGROUND: Mucopolysaccharidosis (MPS) IVA or Morquio A syndrome is a progressive and disabling disease characterized by a deficiency of the enzyme N-acetylgalactosamine-6-sulphate sulphatase. Its clinical presentation ...
  • Norrish, Gabrielle; Cleary, Aoife; Field, Ella; Cervi, Elena; Boleti, Olga; Ziolkowska, Lidia; Olivotto, Iacopo; Khraiche, Diala; Limongelli, Giuseppe; Anastasakis, Aris; Weintraub, Robert; Biagini, Elena; Ragni, Luca; Prendiville, Terence; Duignan, Sophie; McLeod, Karen; Ilina, María; Fernández, Adrián; Marrone, Chiara; Bokenkamp, Regina; Baban, Anwar; Kubus, Peter; Daubeney, Piers-EF; Sarquella-Brugada, Georgia; César, Sergi; Klaassen, Sabine; Ojala, Tiina-H; Bhole, Vinay; Medrano, Constancio; Uzun, Orhan; Brown, Elspeth; Gran, Ferrán; Sinagra, Gianfranco; Castro, Francisco-J; Stuart, Graham; Yamazawa, Hirokuni; Barriales-Villa, Roberto; García-Guereta, Luis; Adwani, Satish; Linter, Katie; Bharucha, Tara; Gonzales-López, Esther; Siles, Ana; Rasmussen, Torsten-B; Calcagnino, Margherita; Jones, Caroline-B; de-Wilde, Hans; Kubo, Toru; Felice, Tiziana; Popoiu, Anca; Mogensen, Jens; Mathur, Sujeev; Centeno, Fernando; Reinhardt, Zdenka; Schouvey, Sylvie; Elliott, Perry-M; Kaski, Juan-Pablo (ELSEVIER SCIENCE INC, 2022-05)
    BACKGROUND: Up to one-half of childhood sarcomeric hypertrophic cardiomyopathy (HCM) presents before the age of 12 years, but this patient group has not been systematically characterized. OBJECTIVES: The aim of this study ...
  • de-Frutos, Fernando; Ochoa, Juan-Pablo; Webster, Gregory; Jansen, Mark; Remior, Paloma; Rasmussen, Torsten-B; Sabater-Molina, María; Barriales-Villa, Roberto; Girolami, Francesca; Cesar, Sergi; Fuentes-Canamero, MEugenia; García-Roves, Reyes-Alvarez; Wahbi, Karim; Limeres, Javier; Kubanek, Milos; Slieker, Martijn-G; Sarquella-Brugada, Georgia; Abrams, Dominic-J; Dooijes, Dennis; Domínguez, Fernando; García-Pavia, Pablo (WILEY, 2024-11)
    BACKGROUND: Although genetic variants in MYH7 are the most frequent cause of pediatric genetic dilated cardiomyopathy (DCM), there are no studies available describing this entity. We sought to describe clinical features, ...
  • Escrihuela-Vidal, Francesc; Eduardo-López-Cortes, Luis; Escola-Verge, Laura; De-Alarcón-González, Aristides; Cuervo, Guillermo; Sánchez-Porto, Antonio; Fernández-Hidalgo, Nuria; Luque, Rafael; Montejo, Miguel; Miro, José-M; Ángel-Goenaga, Miguel; Muñoz, Patricia; Valerio, Maricela; Ripa, Marco; Sousa-Regueiro, Dolores; Gurgui, Merce; Carmen-Farinas-Álvarez, María; Mateu, Lourdes; García-Vázquez, Elisa; Galvez-Acebal, Juan; Carratala, Jordi (OXFORD UNIV PRESS INC, 2021-06)
    BACKGROUND: Although Streptococcus anginosus group (SAG) endocarditis is considered a severe disease associated with abscess formation and embolic events, there is limited evidence to support this assumption. METHODS: We ...
  • Parra, Alejandro; Rabin, Rachel; Pappas, John; Pascual, Patricia; Cazalla, Mario; Arias, Pedro; Gallego-Zazo, Natalia; Santana, Alfredo; Arroyo, Ignacio; Artigas, Merce; Pachajoa, Harry; Alanay, Yasemin; Akgun-Dogan, Ozlem; Ruaud, Lyse; Couque, Nathalie; Levy, Jonathan; Porras-Hurtado, Gloria-Liliana; Santos-Simarro, Fernando; Ballesta-Martínez, María-Juliana; Guillén-Navarro, Encarna; Muñoz-Hernández, Hugo; Nevado, Julián; Tenorio-Castaño, Jair; Lapunzina, Pablo (MDPI, 2023-06)
    SETD2 belongs to the family of histone methyltransferase proteins and has been associated with three nosologically distinct entities with different clinical and molecular features: Luscan-Lumish syndrome (LLS), intellectual ...
  • Proietti, Riccardo; Rivera-Caravaca, José-Miguel; López-Galvez, Raquel; Harrison, Stephanie-L; Buckley, Benjamin-JR; Marin, Francisco; Underhill, Paula; Shantsila, Eduard; Shantsila, Alena; Davies, Rhys; Lane, Deirdre-A; Lip, Gregory-YH (Wiley, 2023-06)
    BACKGROUND: Atrial fibrillation (AF) associates with higher Alzheimer's disease (AD) and vascular dementia risks but the clinical implications have been scarcely investigated. We examined the association between AD or ...
  • Cruz-Utrilla, Alejandro; Gallego-Zazo, Natalia; Antonio-Tenorio-Castaño, Jair; Guillén, Inmaculada; Torrent-Vernetta, Alba; Moya-Bonora, Amparo; Labrandero, Carlos; Garrido-Lestache-Rodríguez-Monte, María-Elvira; Rodríguez-Ogando, Alejandro; del-Mar-Rodríguez-Vázquez-Del-Rey, María; Espin, Juana; Plata-Izquierdo, Beatriz; Álvarez-Fuente, María; Moreno-Galdo, Antonio; Escribano-Subias, Pilar; Del-Cerro-Marin, María-Jesús (MDPI, 2022-09)
    BACKGROUND: Pulmonary arterial hypertension (PAH) is a severe and rare disease with an important genetic background. The influence of genetic testing in the clinical classification of pediatric PAH is not well known and ...
  • Nicola, Andrada-Gabriela; Pricop, Marius-Octavian; Ramos-Medina, Benito (SPRINGERNATURE, 2024-04-23)
    The authors present a case of a 29-year-old female patient with a recurrent submental abscess formation after chin augmentation with highly reticulated hyaluronic acid filler. We evaluate the possible cause of this ...
  • García-Torralba, Esmeralda; Pérez-Ramos, Miguel; Ivars-Rubio, Alejandra; Navarro-Manzano, Esther; Blaya-Boluda, Noel; de-la-Morena-Barrio, Pilar; García-Garre, Elisa; Martínez-Diaz, Francisco; Chaves-Benito, Asunción; García-Martínez, Elena; Ayala-de-la-Peña, Francisco (MDPI, 2023-05)
    Luminal breast cancer (BC) is associated with less immune activation, and the significance of stromal lymphocytic infiltration (sTIL) is more uncertain than in other BC subtypes. The aim of this study was to investigate ...
  • Bernal, Teresa; Fernández-Moreno, Ainhoa; de-LaIglesia, Almudena; Benavente, Celina; García-Noblejas, Ana; García-Belmonte, Daniel; Riaza, Rosalía; Salamero, Olga; Ángeles-Foncillas, María; Roldán, Alicia; Noriega-Concepcion, Víctor; Llorente-González, Laura; Bergua-Burgues, Juan-Miguel; Lorente-de-Una, Soraya; Rodríguez-Macias, Gabriela; de-la-Fuente-Burguera, Adolfo; García-Pérez, María-José; López-Lorenzo, José-Luis; Martínez, Pilar; Alaez, Concepcion; Callejas, Marta; Martínez-Chamorro, Carmen; Rifon-Roca, José; Amador-Barciela, Lourdes; Mena-Durán, Armando-V; Gómez-Correcha, Karoll; Lavilla-Rubira, Esperanza; Amigo, María-Luz; Vall-llovera, Ferrán; Garrido, Ana; García-Fortes, María; de-Miguel-Llorente, Dunia; Aules-Leonardo, Anastasia; Cervero, Carlos; Coll-Jordá, Rosa; Pérez-Encinas, Manuel-Mateo; Polo-Zarzuela, Marta; Figuera, Ángela; Rad, Guillermo; Martínez-Cuadrón, David; Montesinos, Pau (Wiley, 2023-07)
    BACKGROUND: CPX-351 is approved for the treatment of therapy related acute myeloid leukemia (t-AML) and AML with myelodysplastic related changes (MRC-AML). The benefits of this treatment over standard chemotherapy has not ...
  • Moral-Martos, Amadora; Guerrero-Fernández, Julio; GómezBalaguer, Marcelino; Echevarria, Itxaso-Rica; Campos-Martorell, Ariadna; Jesus-Chueca-Guindulain, María; García-García, Emilio; Hoyos-Gurrea, Raúl; López-de-Lara, Diego; Pedro-López-Siguero, Juan; Martos-Tello, José-María; Mora-Palma, Cristina; Riaño-Galán, Isolina; Yeste-Fernández, Diego (EDICIONES DOYMA S A, 2022-04)
  • Esteban-Fernández, Alberto; Recio-Mayoral, Alejandro; López-Vilella, Raquel; de-Lara, Gregorio; Barrantes-Castillo, Moisés; Gómez-Otero, Inés; Nuñez-Villota, Julio; Robles-Gamboa, Carolina; López-Aguilera, José; Iniesta-Manjavacas, Ángel; Fluviá, Paula; Pastor-Pérez, Francisco; Belarte-Tornero, Laia; Alonso-Salinas, Gonzalo; Díez-Villanueva, Pablo (Frontiers Media SA, 2024)
    INTRODUCTION: Vericiguat, an oral stimulator of soluble guanylate cyclase, reduces cardiovascular mortality and hospitalisations in patients with heart failure (HF) and reduced ejection fraction, as demonstrated in the ...
  • Caravaca-Fontan, Fernando; Cavero, Teresa; Diaz-Encarnación, Montserrat; Cabello, Virginia; Ariceta, Gema; Quintana, Luis-F; Marco, Helena; Barros, Xoana; Ramos, Natalia; Rodríguez-Mendiola, Nuria; Cruz, Sonia; Fernández-Juarez, Gema; Rodríguez, Adela; Pérez-de-Jose, Ana; Rabasco, Cristina; Rodado, Raquel; Fernández, Loreto; Pérez-Gómez, Vanessa; Avila, Ana; Bravo, Luis; Espinosa, Natalia; Allende, Natalia; Dolores-Sánchez-de-la-Nieta, María; Rodríguez, Eva; Rivas, Begona; Melgosa, Marta; Huerta, Ana; Miquel, Rosa; Mon, Carmen; Fraga, Gloria; de-Lorenzo, Alberto; Draibe, Juliana; González, Fayna; Shabaka, Amir; López-Rubio, María-Esperanza; Ángeles-Fenollosa, María; Martín-Penagos, Luis; Da-Silva, Iara; Alonso-Titos, Juana; Rodríguez-de-Cordoba, Santiago; Goicoechea-de-Jorge, Elena; Praga, Manuel (AMER SOC NEPHROLOGY, 2023-05)
    KEY POINTS: Kidney survival in C3 glomerulopathy is significantly higher in patients with a disease chronicity score <4 and proteinuria <3.5 g/d, regardless of baseline eGFR. A faster eGFR decline in C3 glomerulopathy is ...